Abstract

The incidence rate of ovarian herniation in the inguinal canal is 3 . Nevertheless, the herniation of ovary with uterus is extremely scarce. Most of these cases are accompanied with congenital genitourinary malformations such as Mayer-Rakitansky-Kuster-Hauser (MRKH) syndrome and Mullerian duct malformations. Herein, a 13-year-old girl presented with type2 MRKH syndrome together with left groin swelling and pain. Sonography reports ovarian herniation into left inguinal canal and magnetic resonance imaging (MRI) confirmed the diagnosis and demonstrated the left ovary, fallopian tube and rudimentary left horn of bicornuate uterus in the left inguinal canal accompanied with ectopic renal of left lower quadrant. Finally, the patient was designed for surgical inguinal exploration and left normal ovary, fallopian tube and rudimentary left horn of bicornuate uterus were replaced in the pelvis.