(2015) Autoimmune lymphoproliferative syndrome misdiagnosed as hemophagocytic lymphohistiocytosis; a case report. Iranian Journal of Blood and Cancer. pp. 198-200. ISSN 20084595 (ISSN)
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Autoimmune lymphoproliferative syndrome misdiagnosed as hemophagocytic lymphohistiocytosis; a case report.pdf Download (459kB) |
Abstract
Autoimmune lymphoproliferative Syndrome (ALPS) is a rare inherited disorder of apoptosis. It usually presents with chronic lymphadenopathy, splenomegaly, and symptomatic cytopenia in a child. Herein, we report a 14-year-old boy with symptoms misdiagnosed as hemophagocytic lymphohistiocytosis who was treated before ALPS was diagnosed for the patient. This case should alert pediatricians to consider ALPS in differential diagnosis of a child with lymphadenopathy, splenomegaly, and cytopenia. © 2015, Iranian Pediatric Hematology and Oncology Society. All rights reserved.
| Item Type: | Article |
|---|---|
| Keywords: | Autoimmune lymphoproliferative syndrome Cytopenia Hemophagocytic lymphohistiocytosis Lymphadenopathy Splenomegaly azathioprine ferritin prednisone adolescent Article case report fever flow cytometry hemophagocytic syndrome human hypersplenism hypofibrinogenemia immunoelectrophoresis male pancytopenia polymerase chain reaction splenectomy |
| Divisions: | |
| Page Range: | pp. 198-200 |
| Journal or Publication Title: | Iranian Journal of Blood and Cancer |
| Journal Index: | Scopus |
| Volume: | 7 |
| Number: | 4 |
| ISSN: | 20084595 (ISSN) |
| Depositing User: | مهندس مهدی شریفی |
| URI: | http://eprints.bmsu.ac.ir/id/eprint/412 |
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